Subacute spongiform encephalopathy (Creutzfeldt-Jakob disease) with amyloid angiopathy.
نویسندگان
چکیده
A case is reported of Creutzfeldt-Jakob disease associated with amyloid infiltration of cerebral vessels. The duration of progressive dementia was only 4 months. Neuritic plaques were not a feature of the pathology. This report emphasises the association of spongiform encephalopathy with the presence of amyloid in the brain.
منابع مشابه
Subacute spongiform encephalopathy and its relation to Jakob-Creutzfeldt disease: report on six cases.
An account is given of six cases of Jakob-Creutzfeldt disease confirmed at necropsy. The rapid fatal outcome within three months was typical of the variety designated subacute spongiform encephalopathy (Nevin-Jones). The characteristic EEG changes were found to be of great value in making an early diagnosis and, together with akinetic mutism and myoclonus, constituted an easily recognizable pic...
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عنوان ژورنال:
- Journal of neurology, neurosurgery, and psychiatry
دوره 48 11 شماره
صفحات -
تاریخ انتشار 1985